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KMID : 0358920080350020319
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Journal of the Korean Academy of Pedodontics
2008 Volume.35 No. 2 p.319 ~ p.323
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EDWARDS SYNDROME : REPORT OF A CASE
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Park Ji-Eun
Kim Seung-Oh
Kim Jong-Soo
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Abstract
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Edward’s syndrome is a genetic disorder of 18th chromosomal trisomy. Main clinical features of this syndrome include systemic conditions, such as mental retardation, growth retardation, dyspnea, congenital heart disease, and orthopedic disorders, such as flexion deformity and rocker-bottom feet. The characteristics of fetal abnormality are hydramnios, small placenta, common umbilical artery. Infants with Edward’s syndrome have very low survival rate. Almost half of them die during fetal stage. Fifty percent of them survive 2 months, and 5 to 10 percent of them survive about 1 year. A 3-year and 7 month old girl visited our dental hospital for the treatment of dental caries. Considering her systemic disease, low body weight, medical history of cardiac surgery, and difficulty in airway management, dental procedure was performed under general anesthesia. We report this case with review of literatures.
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KEYWORD
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Edwards syndrome, Trisomy 18
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